000			04039nam a22005295i 4500
001			u372542
003			SIRSI
005			20160812084103.0
007			cr nn 008mamaa
008			100721s2010 xxu| s |||| 0|eng d
020			_a9781603275248 _9978-1-60327-524-8
040			_cMX-MeUAM
050		4	_aRC799-869
082	0	4	_a616.33 _223
100	1		_aMurray, Karen F. _eeditor.
245	1	0	_aFibrocystic Diseases of the Liver _h[recurso electrónico] / _cedited by Karen F. Murray, Anne M. Larson.
264		1	_aTotowa, NJ : _bHumana Press, _c2010.
300			_aXII, 640p. 161 illus., 70 illus. in color. _bonline resource.
336			_atext _btxt _2rdacontent
337			_acomputer _bc _2rdamedia
338			_aonline resource _bcr _2rdacarrier
347			_atext file _bPDF _2rda
490	1		_aClinical Gastroenterology
505	0		_aPathophysiology and Development -- Embryology and Development of the Ductal Plate -- Cholangiocyte Biology as Relevant to Cystic Liver Diseases -- Cholangiocyte Cilia and Basal Bodies -- Genetics of Fibrocystic Diseases of the Liver and Molecular Approaches to Therapy -- Diagnosis -- Radiologic Findings in the Fibrocystic Diseases -- Pathology of Fibrocystic Diseases of the Liver -- Disease States -- Alagille Syndrome and JAGGED1/NOTCH Sequence -- Biliary Atresia and the Ductal Plate -- Nephronophthisis and Renal–Hepatic–Pancreatic Dysplasia of Ivemark -- Meckel and Joubert Syndromes -- Bardet–Biedl and Jeune Syndromes -- Congenital Disorders of Glycosylation and Their Effects on the Liver -- Autosomal Recessive Polycystic Kidney Disease -- Caroli Disease, Caroli Syndrome, and Congenital Hepatic Fibrosis -- Simple Hepatic Cysts/Choledochal Cysts -- Autosomal Dominant Polycystic Liver Disease -- Echinococcal/Hydatid Cysts of the Liver -- Miscellaneous Cystic Lesions of the Liver -- Complications -- Vascular Complications of Fibrocystic Liver Disease -- Biliary Cystadenoma and Cystadenocarcinoma -- Cholangitis -- Surgical Management -- Surgical Management of Fibrocystic Liver Disease.
520			_aIn recent years there have been huge advances in the understanding of the genetic and molecular basis of the fibrocystic diseases. This volume provides a thorough review of fibrocyctic diseases that affect the liver. It contains in-depth discussions of the genetics, molecular biology, pathogenesis, histology, clinical presentations, complications of, treatment, and prognosis of the conditions affecting children and adults, and hence will be the gold-standard reference for these conditions. In addition, the histological features that distinguish these conditions from other potentially fibrosing hepatopathies are illustrated. Conditions with syndromic features involving the kidney or other organ systems are also reviewed. Thorough review of the clinical phenotypes, their presentations, treatment, potential complications of, and prognosis is discussed. Fibrocystic Diseases of the Liver will be an invaluable resource for hepatologists, gastroenterologists, nephrologists, and hepatic surgeons who care for children and adults with liver disease, as well as basic scientists in molecular genetics, hepatobiliary pathophysiology, hepatology and nephrology.
650		0	_aMedicine.
650		0	_aGastroenterology.
650		0	_aClinical medicine.
650		0	_aNephrology.
650		0	_aPediatrics.
650		0	_aAbdomen _xSurgery.
650	1	4	_aMedicine & Public Health.
650	2	4	_aGastroenterology.
650	2	4	_aHepatology.
650	2	4	_aNephrology.
650	2	4	_aPediatrics.
650	2	4	_aAbdominal Surgery.
700	1		_aLarson, Anne M. _eeditor.
710	2		_aSpringerLink (Online service)
773	0		_tSpringer eBooks
776	0	8	_iPrinted edition: _z9781603275231
830		0	_aClinical Gastroenterology
856	4	0	_zLibro electrónico _uhttp://148.231.10.114:2048/login?url=http://link.springer.com/book/10.1007/978-1-60327-524-8
596			_a19
942			_cLIBRO_ELEC
999			_c200422 _d200422